Primary Tracheal Epithelioid Angiosarcoma - Uncommon Tumor at an Uncommon Site

We report a rare case of an elderly gentleman presenting with hemoptysis and stridor secondary to a primary tracheal EpithelioidAngiosarcoma (EAS). EAS continues to be a rare clinical entity with its occurrence in the trachea having been described only twice before to our knowledge. This case also demonstrates the importance of Immunochemistry in accurately making a diagnosis of EAS as the epithelioid features mimic other epithelial tumors like adenocarcinomas. In the absence of definitive guidelines, treatment decisions are often made on a case-by-case basis. The inability to perform surgical resection led to a poor outcome in our patient with second-line radiation therapy failing to achieve remission.